What is Hemophilia?

Hemophilia comes from Ancient Greek, which consists of two words namely haima which means blood and philia which means love or affection.
Hemophilia is an inherited disease, which means it is passed down from mother to child when the child is born.


Blood in a hemophilia sufferer cannot freeze itself normally. The process of blood clotting in a person with hemophilia is not as fast and as much as other normal people. He will need more time for his blood clotting process.
Most people with hemophilia experience bleeding disorders under the skin; such as bruising if you experience a slight impact, or bruising arises by itself if the patient has carried out strenuous activities; swelling of the joints, such as wrinkles, ankles or elbows. The suffering of hemophilia sufferers can endanger their soul if bleeding occurs in vital parts of the body such as bleeding in the brain.
Hemophilia A and B
Hemophilia is divided into two types, namely:
Hemophilia A, also known as:
• Hemophilia Classic: Because this type of hemophilia is the most lacking of clotting factors in the blood.
• Hemophilia lacks Factor VIII: Occurs due to lack of factor 8 (Factor VIII) protein in the blood which causes problems in the blood clotting process.
Hemophilia B was also known as:
• Christmas Disease: Because it was discovered for the first time in a person named Steven Christmas from Canada
• Hemophilia lacks Factor IX: Occurs due to lack of factor 9 (Factor IX) protein in the blood which causes problems in the blood clotting process.
How can blood clotting disorders occur?
The disorder can occur because the amount of certain types of blood clots is less than the normal number, even almost none — the difference in the process of blood clotting that occurs between ordinary people and hemophilia patients.

The blood clotting process that occurs in normal people:
• When experiencing bleeding means there is a wound in a blood vessel (i.e. a channel where blood flows throughout the body), then blood comes out of the vessels.
• Blood vessels shrink/shrink.
• Blood platelets (platelets) will cover wounds in the vessels.
• Blood clotting factors work to make wicker (fibrin threads) that will close the wound so that the blood stops flowing out of the vessels.
The blood clotting process that occurs in hemophiliacs:
• When experiencing bleeding means there is a wound in a blood vessel (ie a channel where blood flows throughout the body), then blood comes out of the vessels.
• Blood vessels shrink/shrink.
• Blood platelets (platelets) will cover wounds in the vessels.
• Lack of a number of certain blood clotting factors, resulting in woven wounds not forming correctly, so that blood does not stop flowing out of the vessels.
F.A. Hemophilia
How many hemophilia sufferers are found?
Hemophilia A or B is a rare disease. Hemophilia A occurs at least 1 in 10,000 people. Hemophilia B is less common, which is 1 in 50,000 people.
Who can experience hemophilia?
Hemophilia does not recognize race, skin color or ethnicity.
Hemophilia is mostly suffered only in men. A woman will experience hemophilia if her father is hemophilia and her mother is carrying a carrier. Moreover, this is very rare. (See Decreased Hemophilia)
As a lowered disease, people will be exposed to hemophilia since he was born, but in fact hemophilia is always detected in the first year of his birth.
Hemophilia level
Hemophilia A and B can be classified into 3 levels, namely:
Classification of Factor VII Levels and Factor IX in the blood
Weightless than 1% of the normal amount
Medium 1% – 5% of the normal amount
Lightweight 5% – 30% of the normal amount

Severe/severe hemophilia sufferers who only have factor VIII levels or factor IX less than 1% of the normal amount in their blood, can experience several bleeding times in a month. Sometimes bleeding just happens for no apparent reason.
People with moderate hemophilia are less bleeding than severe hemophilia. Bleeding sometimes occurs due to body activity that is too heavy, such as excessive exercise.
People with mild hemophilia are less likely to experience bleeding. They experience bleeding problems only in certain situations, such as surgery, tooth extraction or serious injury. Mild hemophilia women may experience more bleeding during menstruation.

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